Tetralogy of Fallot with absent pulmonary valve syndrome : a 34-year African single centre experience
Background: Absent pulmonary valve syndrome (APVS) is most commonly associated with Tetralogy of Fallot (TOF).TOF with APVS is characterised by features of TOF with either rudimentary ridges or complete absence of pulmonary valve tissue.This is often associated with varying degrees of pulmonary stenosis and severe pulmonary regurgitation with massi